Abstract

*L. Dehou, A. Lamine, M. Lahlali, A. El Mekkaoui N. Lahmidani, M. El Yousfi, D. A. Benajah, M. ElAbkari A. Ibrahimi and H. Abid

ABSTRACT

Primary intestinal lymphangiectasia or Waldmann's disease is due to lymphatic dilatation with leakage of lymph into the intestinal lumen responsible for hypoprotidemia, chronic diarrhea due to exudative enteropathy, and edema.It is a disease usually revealing itself in childhood, sometimes with growth retardation in severe forms and of which there are some familial forms. While edema is common in Waldmann's disease and is related to hypoproteinemia, lymphedema is less common but can affect the lower and upper limbs(1). In the course of the disease, they usually occur after the digestive involvement which is symptomatic and in the foreground. We report a case of lymphoedema of the limbs evolving for several years and considered as primary, before the diagnosis of paucisymptomatic Waldmann disease was made.