NON-COMPACTION OF THE FAMILY LEFT VENTRICLE ABOUT TWO CASES FROM THE SAME FAMILY AND REVIEWED LITERATURE
Dania Srifi*, Pr. Nadia Fellat and Pr. Roukaya Fellat
ABSTRACT
Isolated non-compaction of the left ventricle (NCVG) is a rare congenital cardiomyopathy resulting from the shutdown of normal embryogenesis of the myocardium. Its main feature is the existence of many deep heart-related ventricular trabeculations, generally located at the level of the apex of the left ventricle. Diagnosis is based on echocardiography and magnetic resonance imaging (MRI), and may be difficult in the atypical forms. The clinical presentation and the prognosis are very variable. Familial forms are not rare, ordering a family screening.[1,2] We report the case of a young patient admitted in a context of global heart failure related to NCVG and whose screening of first-degree relatives has highlighted the same pathology in the mother who is clinically asymptomatic.
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