Abstract

Dr. A. Mennouni*, H. Ngham, H. Ardhaoui, S. Rouadi, R. Abada, M. Roubal and M. Mahtar

ABSTRACT

The association of otosclerosis with a Malleus ankylosis called goodhill syndrome is very rare, accounting for less than 1% of congenital malformations of the middle ear.[1] We report the case of a 46-year-old woman with no family history of deafness who had been consulting for bilateral deafness, evolving for 10 years, with no associated signs such as vertigo or tinnitus. Otoscopic examination show normal eardrums, The audiogram includes a conductive hearing loss of 60 dB d. Computed tomography is the main examination for the visualization of the ossicular chain and the search for other anomalies. The diagnosis is confirmed during the surgery. We have reported a case of bilateral Malleus ankylosis associated with otosclerosis. This makes our study interesting because it is rarely described in the literature. The objective of this study was to analyze the findings of middle ear exploration and the frequency of ossicular in patients with suspected otosclerosis. bone bridge (Figure 1). The surgery consists of an ossiculoplasty, by section of Malleus's neck with interposition with Incus. We obtained a good result by gain of 20 dB in the main frequency. Our patient is satisfied. The other side will be programmed a year later.